What is Urticaria Pigmentosa (Mastocytosis of the skin)?
Urticaria Pigmentosa (UP) is an uncommon rash that affects the skin of infants, children and young adults. The rash is made up of reddish-brown spots called mastocytomas that are flat or slightly raised and may form hives when they are rubbed or scratched. Sometimes the spots will blister. There may be a few spots or many spots. The lesions usually are most prominent on the trunk, but can occur on the scalp, face and extremities.
How does UP affect your child?
The rash of UP is not painful but does cause itching in some children. Massive histamine release can cause headaches, flushing (redness of the skin), diarrhea, vomiting, wheezing (breathing hard with a whistling sound), increased heart rate and a decrease in blood pressure. These symptoms are rarely observed in young children with UP. Please let your doctor know if your child experiences any of these symptoms.
How long does UP last?
Most infants and children will outgrow UP as they get older. New spots may continue to appear as long as the condition lasts. There is no known treatment to prevent new spots from appearing. The reddish-brown spots may fade as your child grows older but usually last for years.
In some cases your doctor may suggest the following:
Your child’s primary care doctor, dentist, child care provider and school be provided with a copy of this information. You may also want to keep a copy of this information in your car or purse in case of emergency.
Your child wear a medical alert bracelet that reads: “Urticaria Pigmentosa (Mastocytosis).”
If your child has surgery or visits the emergency room, the doctors be informed of your child’s UP and given a copy of this information.